Journal of Electrocardiology
Volume 42, Issue 2 , Pages 136.e1-136.e5 , March 2009

The electrocardiogram in right ventricular cardiomyopathy/dysplasia. How can the electrocardiogram assist in understanding the pathologic and functional changes of the heart in this disease?

  • Frank I. Marcus, MD

      Affiliations

    • Sarver Heart Center, Tucson, AZ, USA
    • Corresponding Author InformationCorresponding author. Tel.: +1 520 626 1416; fax: +1 520 626 4333.
    • ,
  • Wojciech Zareba, MD

      Affiliations

    • Heart Research Follow-up Program, Cardiology Unit, University of Rochester, Box 653, Rochester, NY, USA

Received 11 November 2008

References 

  1. Nava A, Buja G, Corrado D. Electrocardiographic features. In:  Nava A,  Rossi G,  Thiene G editor. Arrhythmogenic right ventricular cardiomyopathy/dysplasia. Amsterdam, The Netherlands: Elsevier Science; 1997;p. 186
  2. Zareba W, Piotrowicz K, Turrini P. Electrocardiographic manifestations. In:  Marcus FI,  Nava A,  Thiene G editor. Arrhythmogenic right ventricular cardiomyopathy/dysplasia. Milan, Italy: Springer-Verlag; 2007;p. 121
  3. Durrer D, Van Dam THR, Freud GE, Janse MJ, Meijler FL, Arzbaecher RC. Total excitation of the isolated human heart. Circulation. 1970;16:899
  4. Fontaine G, Guiraudon G, Frank R. Intramyocardial conduction defects in patients prone to chronic ventricular tachycardia. I. The post-excitation syndrome in sinus rhythm. In:  Sandoe E,  Julian DG,  Bell JW editor. Management of ventricular tachycardia—role of mexilitine. Amsterdam, The Netherlands: Exerpta Medica; 1978;p. 39
  5. McKenna WJ, Thiene G, Nava A, et al. Diagnosis of arrhythmogenic right ventricular dysplasia, cardiomyopathy. Br Heart J 71:215.
  6. Marcus FI, Fontaine GH, Guiraudon G, Frank R, Laurenceau JL, Malergue C, et al. Right ventricular dysplasia: a report of 24 adult cases. Circulation. 1982;65:384
  7. Marcus FI. Prevalence of T wave inversion beyond V1 in young normal individuals and usefulness for the diagnosis of arrhythmogenic right ventricular cardiomyopathy/dysplasia. Am J Cardiol. 2005;95:1070
  8. Nava A, Canciani B, Buja G, et al. Electrovectorcardiographic study of negative T waves on precordial leads in arrhythmogenic right ventricular dysplasia: relationship with right ventricular volumes. J Electrocardiol. 1988;21:239
  9. Jaoude SA, Leclercq JF, Coumel P. Progressive ECG changes in arrhythmogenic right ventricular disease. Evidence for an evolving disease. Eur Heart J. 1996;17:1717
  10. Peters S, Trummel M. Diagnosis of arrhythmogenic right ventricular dysplasia-cardiomyopathy: value of standard ECG revisited. ANE. 2003;8:238
  11. Nasir K, Bomma C, Tandri H, et al. Electrocardiographic features of arrhythmogenic right ventricular dysplasia/cardiomyopathy according to disease severity. A need to broaden diagnostic criteria. Circulation. 2004;110:1527
  12. Dalal D, Nasir K, Bomma C, et al. Arrhythmogenic right ventricular dysplasia: a United States experience. Circulation. 2005;112:3823
  13. Cox MGPJ, Nelen MR, Wilde AAM, et al. Activation delay and VT parameters in arrhythmogenic right ventricular dysplasia/cardiomyopathy: toward improvement of diagnostic ECG criteria. J Cardiovasc Electrophysiol. 2008;19:775
  14. Niroomand F, Carbucicchio C, Tondo C, et al. Electrophysiological characteristics and outcome in patients with idiopathic right ventricular arrhythmia compared with arrhythmogenic right ventricular dysplasia. Heart. 2002;87:41
  15. O'Donnell D, Cox D, Bourke J, Mitchell L, Furniss S. Clinical and electrophysiological differences between patients with arrhythmogenic right ventricular dysplasia and right ventricular outflow tract tachycardia. Eur Heart J. 2003;24:801
  16. Proclemer A, Ciani R, Feruglio GA. Right ventricular tachycardia with left bundle branch block and inferior axis morphology: clinical and arrhythmological characteristics in 15 patients. PACE. 1989;12:977
  17. Ainsworth CD, Skanes AC, Klein GJ, Gula LJ, Yee R, Krahn AD. Differentiating arrhythmogenic right ventricular cardiomyopathy from right ventricular outflow tract ventricular tachycardia using multilead QRS duration and axis. Heart Rhythm. 2006;3:416
  18. Marcus FI, Zareba W, Sherrill D. Evaluation of the normal values for signal averaged electrocardiogram. J Cardiovasc Electrophysiol. 2007;18:231
  19. Nava A, Folino AF, Bauce B, et al. Signal averaged electrocardiogram in patients with arrhythmogenic right ventricular dysplasia. Prevalence, diagnostic and prognostic values. Eur Heart J. 1993;14(Suppl E):80
  20. Nasir K, Tandri H, Rutberg J, et al. Filtered QRS duration on signal averaged electrocardiographic predicts inducibility of ventricular tachycardia in arrhythmogenic right ventricle dysplasia. PACE. 2003;26:1055
  21. Turrini P, Corrado D, Basso C, Nava A, Thiene G. Noninvasive risk stratification in arrhythmogenic right ventricular cardiomyopathy. ANE. 2003;8:161
  22. Hamid MS, Norman M, Quraishi A, et al. Prospective evaluation of relatives for familial arrhythmogenic right ventricular cardiomyopathy/dysplasia reveals a need to broaden diagnostic criteria. J Am Coll Cardiol. 2002;40:1445

PII: S0022-0736(08)00499-8

doi: 10.1016/j.jelectrocard.2008.12.011

Journal of Electrocardiology
Volume 42, Issue 2 , Pages 136.e1-136.e5 , March 2009

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